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Angeborene Herzfehler mit Anomalien des rechtsventrikulären Ausflusstrakts

  • Chapter
Herzchirurgie

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Zusammenfassung

Seit der Beschreibung einer Herzfehlerkombination mit

  • Ventrikelseptumdefekt (VSD),

  • Pulmonalstenose,

  • dextroponierter Aorta (den VSD „überreitend“) und

  • Hypertrophie des rechten Ventrikels

durch Etiennne Louis (1888), zu diesem Zeitpunkt Professor für Hygiene und Gerichtsmedizin in Marseille, ist diese als Fallot-Tetralogie in die medizinische Nomenklatur eingegangen und bis heute als solche geläufig. Eine kommentierte neue Übersetzung der Originalpublikation ins Englische wurde 1989 von Van Praagh herausgebracht. Fallot war jedoch nicht der erste, der auf diesen Herzfehler hinwies. Eine Beschreibung aus dem Jahre 1672 liegt von Stensen vor. Im Jahre 1777 berichtete Sandifort über diese Fehlbildung. Erst Fallot aber stellte die klinisch-pathologische Bedeutung bei solchen Fällen heraus. Als gemeinsames Kennzeichen hob er die Blausucht hervor und sprach ausdrücklich von einer „maladie bleu“.

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Literatur

  • Abella RF, De La Torre T, Mastropietro G et al. (2004) Primary repair of pul monary atresia with ventricular septal defect and major aortopulmonary collaterals: a useful approach. J Thorac Cardiovasc Surg 127:193–202

    PubMed  Google Scholar 

  • Abbot ME (1936) Atlas of congenital heart disease. American Heart Association, New York

    Google Scholar 

  • Acherman RJ, Smallhorn JF, Freedom RM (1996) Echocardiographic as sessment of pulmonary blood supply in patients with pulmonary atresia and ventricular septal defect. J Am Coll Cardiol 28: 1308–1313

    CAS  PubMed  Google Scholar 

  • Alsoufi B, Williams WG, Hua Z et al. (2007) Surgical outcomes in the treat ment of patients with tetralogy of Fallot and absent pulmonary valve. Eur J Cardiothorac Surg 31: 354–359

    PubMed  Google Scholar 

  • Alva C, Ho SY, Lincoln CR et al. (1999) The nature of the obstructive muscular bundles in double-chambered right ventricle. J Thorac Cardiovasc Surg 117: 1180–1189

    CAS  PubMed  Google Scholar 

  • Alwi M, Geetha K, Bilkis AA et al. (2000) Pulmonary atresia with intact ventricular septum percutaneous radiofrequency-assisted vagot omy and balloon dilation versus surgical valvotomy and Blalock Taussig shunt. J Am Coll Cardiol 35: 468–476

    CAS  PubMed  Google Scholar 

  • Anderson RH, Becker AE, Wilcox BR, Macartney FJ, Wilkinson JL (1983) Surgical anatomy of double-outlet right ventricle — a reappraisal. Am J Cardiol 52: 555–559

    CAS  PubMed  Google Scholar 

  • Anderson RH, Devine WA, Del Nido P (1991) The surgical anatomy of tetralogy of Fallot with pulmonary atresia rather than pulmonary stenosis. J Card Surg 6: 41–58

    CAS  PubMed  Google Scholar 

  • Aoki M, Forbess JM, Jonas RA, Mayer JE Jr, Castaneda AR (1994) Result of biventricular repair for double-outlet right ventricle. J Thorac Cardiovasc Surg 107: 338–349

    CAS  PubMed  Google Scholar 

  • Arai N, Matsumoto A, Nishikawa N et al. (2001) Beta-blocker therapy improved symptoms and exercise capacity in a patient with dy namic intra-right ventricular obstruction: an atypical Form of double-chambered right ventricle. J Am Soc Echocardiogr 14: 650–653

    CAS  PubMed  Google Scholar 

  • Atallah-Yunes NH, Kavey RE, Bove EL et al. (1996) Postoperative assess ment of a modified surgical approach to repair of tetralogy of Fallot. Long-term follow-up. Circulation 94: 1122–1126

    Google Scholar 

  • Bacha EA, Scheule AM, Zurakowski D et al. (2001) Long-term results after early primary repair of tetralogy of Fallot. J Thorac Cardiovasc Surg 122: 14–61

    Google Scholar 

  • Barbero-Marcial M, Tamanati C, Jatene MB et al. (1998) Double-outlet right ventricle with nonrelated ventricular septal defect: surgical results using the multiple patches technique. Heart Surg Forum 1: 125–129

    CAS  PubMed  Google Scholar 

  • Bautista-Hernandez V, Kaza AK, Benavidez OJ, Pigula FA (2008) True an eurysmal dilatation of a contegra conduit after right ventricular outflow tract reconstructions novel mechanism of conduit failure. AnnThorac Surg 86: 1976–1977

    Google Scholar 

  • Belli E, Serraf A, Lacour-Gayet F et al. (1998) Biventricular repair for dou ble-outlet right ventricle. Results and long-term follow-up. Circulation 98: II360–II365

    CAS  PubMed  Google Scholar 

  • Berdat PA, Carrel T (2006) Off-pump pulmonary valve replacement with the new Shelhigh Injectable Stented Pulmonic Valve. J Thorac Cardiovasc Surg 131: 1192–1193

    PubMed  Google Scholar 

  • Blalock A, Taussig HB (1949) The surgical management of the malformation of the heart in which there is pulmonary stenosis or atresia. JAMA 128: 189

    Google Scholar 

  • Bonhoeffer P, Boudjemline Y, Saliba Z et al.(2000) Percutaneous replacement of pulmonary valve in a right-ventricle to pulmonary-artery prosthetic conduit with valve dysfunction. Lancet 356: 1403–1405

    CAS  PubMed  Google Scholar 

  • Bove EL, Shaher RM, Alley R, McKneally M (1972) Tetralogy of Fallot with absent pulmonary valve and aneurysm of the pulmonary artery: report of two cases presenting as obstructive lung disease. J Pediatr 81: 339–343 417–420

    CAS  PubMed  Google Scholar 

  • Brandt PW, Calder AL, Barratt-Boyes BG, Neutze JM (1976) Double outlet left ventricle. Morphology, cineangiocardiographic diagnosis and surgical treatment. Am J Cardiol 38:897–909

    CAS  PubMed  Google Scholar 

  • Brizard CP, Mas C, Sohn YS, Cochrane AD, Karl TR (1998) Transatrialtranspulmonary tetralogy of Fallot repair is effective in the presence of anomalous coronary arteries. J Thorac Cardiovasc Surg 116: 770–779

    CAS  PubMed  Google Scholar 

  • Brock R (1948) Pulmonary valvotomy for the relief of congenital pulmonary stenosis. Br Med J 1:1121

    CAS  PubMed  Google Scholar 

  • Brown JW, Ruzmetov M, Rodefeld M D, Vijay P, Darragh RK (2006) Valved bovine jugular vein conduits for right ventricular outflow tract reconstruction in children; an attractive alternative to pulmonary homograft. Ann Thorac Surg 82:909–916

    PubMed  Google Scholar 

  • Brown JW, Ruzmetov M, Vijay P, Rodefeld M D, Turrentine M W (2007) Right ventricular outflow tract reconstruction with a polytetrafluoroethylene monocusp valve: a twelve-year experience. J Thorac Cardiovasc Surg 133:1336–1343

    PubMed  Google Scholar 

  • Bryant R 3rd, Nowicki ER, Mee RB et al. (2008) Success and limitations of right ventricular sinus myectomy for pulmonary atresia with intact ventricular septum. J Thorac Card iovasc Surg 136:735–742

    Google Scholar 

  • Bull C, de Levai MR, Mercanti C, Macartney FJ, Anderson RH (1982) Pulmonary atresia and intact ventricular septum: a revised classification. Circulation 66:266–272

    CAS  PubMed  Google Scholar 

  • Castaneda AR, Freed MD, Williams RG, Norwood WI (1977) Repair of tetralogy of Fallot in infancy. Early and late results. J Thorac Cardiovasc Surg 74:372–381

    CAS  PubMed  Google Scholar 

  • Cooley DA, Hallman GL (1966) Intra pericardial aortic-right pulmonary arterial anastomosis. Surg Gynecol Obstet 122:1084–1086

    CAS  PubMed  Google Scholar 

  • Davignon AL, Greenwold WE, DuShane JW, Edwards JE (1961) Congenital pulmonary atresia with intact ventricular septum. Clinicopathologic correlation of two anatomic types. Am Heart J 62:591–602

    CAS  PubMed  Google Scholar 

  • deLeval MR, McKay R, Jones M, Stark J, Macartney FJ (1981) Modified Blalock-Taussig shunt. Use of subclavian artery orifice as flow regulator in prosthetic systemic-pulmonary artery shunts. J Thorac Cardiovasc Surg 81:112–119

    CAS  Google Scholar 

  • Delius RE, Rademecker MA, de Levai MR, Elliott MJ, Stark J (1996) Is a high-risk biventricular repair always preferable to conversion to a single ventricle repair? J Thorac Cardiovasc Surg 112:1561–1568

    CAS  PubMed  Google Scholar 

  • del Nido PJ (2006) Surgical management of right ventricular dysfunction late after repair of tetralogy of fallot: right ventricular remodeling surgery. Semin Thorac Card iovasc Surg Pediatr Card Surg Annu: 29–34

    Google Scholar 

  • Di Donato RM, Jonas RA, Lang P, Rome JJ, Mayer JE Jr, Castaneda AR (1991) Neonatal repair of tetralogy of Fallot with and without pulmonary atresia. J Thorac Cardiovasc Surg 101:126–137

    PubMed  Google Scholar 

  • Dodge-Khatami A, Backer CL, Holinger LD, Baden HP, Mavroudis C (1999) Complete repair of tetralogy of Fallot with absent pulmonary valve including the role of airway stenting. J Card Surg 14: 82–91

    CAS  PubMed  Google Scholar 

  • Doty DB (1986) Correction of Taussig-Bing malformation by intraventricular conduit. J Thorac Cardiovasc Surg 91:133–138

    CAS  PubMed  Google Scholar 

  • d’Udekem Y, Alphonso N, Nørgaard MA et al. (2005) Pulmonary atresia with ventricular septal defects and major aortopulmonary collateral arteries: unifocalization brings no long-term benefits. J Thorac CardiovascSurg 130:1496–1502

    Google Scholar 

  • Edmunds LH Jr, Saxena NC, Friedman S, Rashkind WJ, Dodd PF (1976) Transatrial repair of tetralogy of Fallot. Surgery 80:681–688

    PubMed  Google Scholar 

  • Emmanouilides G, Thanopoulos B, Siassi B et al. (1978) Agenesis of ductus arteriosus associated with the syndrome of tetralogy of Fallot and absent pulmonary valve. Am J Cardiol 37:404–409

    Google Scholar 

  • Fallot EL (1888) Contribution a l’anatomie pathologique de la maladie bleue (cyanose cardia que). Marseille Med 25:77, 138, 207, 341, 403

    Google Scholar 

  • Foker JE, Setty SP, Berry J et al. (2008) Treatment of right ventricle to coronary artery connections in infants with pulmonary atresia and intact ventricular septum. J Thorac Cardiovasc Surg 136:749–756

    PubMed  Google Scholar 

  • François K, Zaquot M, Bové T, Vandekerckhove K, De Groote K, Panzer J, De Wilde H, De Wolf D (2009) Vortrag auf der 23. Jahrestagung European Association for Cardio-Thoracic Surgery, Wien 20. Oktober 2009

    Google Scholar 

  • Fraser CD Jr, Latson LA, Mee RB (1995) Surgical repair of severe bilateral branch pulmonary artery stenosis, Ann Thorac Surg 59:738–740

    PubMed  Google Scholar 

  • Freedom RM, Anderson RH, Perrin D (2005) The significance of ventriculo-coronary arterial connections in the setting of pulmonary atresia with an intact ventricular septum. Cardiol Young 15:447–468

    PubMed  Google Scholar 

  • Freeman JE, DeLeon SY, Lai S, Fisher EA, Ow EP, Pifarré R (1993) Right ventricle-to-aorta conduit in pulmonary atresia with intact ventricular septum and coronary sinusoids. Ann Thorac Surg 56:1393–1395

    CAS  PubMed  Google Scholar 

  • Fyler DC (1992) Tetralogy of Fallot. In: Fyler DC (ed) Nada’s pediatric cardiology. p472. Hanley & Beltus, Philadelphia; Mosby Year Book, St. Louis Baltimore Boston Chicago London Philadelphia Sydney Toronto

    Google Scholar 

  • Gatzoulis MA, Clark AL, Cullen S, Newman CG, Redington AN (1995a) Right ventricular diastolic function 15 to 35 years after repair of tetralogy of Fallot. Restrictive physiology predicts superior exercise performance. Circulation 91:1775–1781

    CAS  PubMed  Google Scholar 

  • Gatzoulis MA, Till JA, Somerville J, Redington AN (1995b) Mechanoelectrical interaction in tetralogy of Fallot. QRS prolongation relates to right ventricular size and predicts malignant ventricular arrhythmias and sudden death. Circulation 92:231–237

    CAS  PubMed  Google Scholar 

  • Giglia TM, Mandell VS, Connor AR, Mayer JE Jr, Lock JE (1992) Diagnosis and management of right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum. Circulation 86:1516–1528

    CAS  PubMed  Google Scholar 

  • Gittenberger-de Groot AC, Sauer U, Bindl L et al. (1988) Competition of coronary arteries and ventriculo-coronary arterial communications in pulmonary atresia with intact ventricular septum. Int J Cardiol 18:243–258

    CAS  PubMed  Google Scholar 

  • Gittenberger-de Groot AC, Sauer U, Oppenheimer-Dekker A, Quaegebeur JM (1983) Coronary arterial anatomy in transposition of the great arteries: A morphology study. Pediatr Cardiol 4 (Suppl 1): 15–24

    Google Scholar 

  • Goor DA, Lillehei CW (1975) Congenital malformations of the heart. Grune & Stratton, New York

    Google Scholar 

  • Griselli M, McGuirk SP, Winlaw DS et al. (2004) The influence of pulmonary artery morphology on the results of operations for major aortopulmonary collateral arteries and complex congenital heart defects. J Thorac Cardiovasc Surg 127:251–258

    PubMed  Google Scholar 

  • Gundry SR, Razzouk AJ, Boskind JF, Bansal R, Bailey LL (1994) Fate of the pericardial monocusp pulmonary valve for right ventricular outflow tract reconstruction. Early function, late failure without obstruction. J Thorac Cardiovasc Surg 107:908–912

    CAS  PubMed  Google Scholar 

  • Hanley FL, Sade R M, Blackstone EH et al. (1993) Outcomes in neonatal pulmonary atresia with intact ventricular septum. A multiinstitutional study. J Thorac Cardiovasc Surg 105:406–423

    CAS  PubMed  Google Scholar 

  • Hartman AF, Goldring D, Carlsson E (1964) Development of right ventricular aberrant muscular bands. Circulation 30:679–685

    Google Scholar 

  • Hausdorf G, Grävinghoff L, Keck EW (1987) Effects of persisting myocardial sinusoids on left ventricular performance in pulmonary atresia with intact ventricular septum. Eur Heart J 8:291–296

    CAS  PubMed  Google Scholar 

  • Haworth SG (1990) Pulmonary vascular development. In: Long WA (ed) Fetal and neonatal cardiology. WB Saunders, Philadelphia, pp 51–63

    Google Scholar 

  • Heinemann MK, Hanley FL (1993) Preoperative management of neonatal tetralogy of Fallot with absent pulmonary valve syndrome. Ann Thorac Surg 55:172–174

    CAS  PubMed  Google Scholar 

  • Hew CC, Daebritz SH, Zurakowski D, del Nido PI, Mayer JE Jr, Jonas RA (2002) Valved homograft replacement of aneurysmal pulmonary arteries for severely symptomatic absent pulmonary valve syndrome. AnnThorac Surg 73:1778–1785

    Google Scholar 

  • Hirsch JC, Mosca RS, Bove EL (2000) Complete repair of tetralogy of Fallot in the neonate: results in the modern era. Ann Surg 232:508–514

    CAS  PubMed  Google Scholar 

  • Hoffman P, Wójcik AW, Rózański J (2004) The role of echocardiography in diagnosing double chambered right ventricle in adults. Heart 90: 789–793

    CAS  PubMed  Google Scholar 

  • Hraska V (2000) A new approach to correction of tetralogy of Fallot with absent pulmonary valve. Ann Thorac Surg 69:1601–1602

    CAS  PubMed  Google Scholar 

  • Hudspeth AS, Cordall AR, Johnston FR (1963) Transatrial approach to total correction of tetralogy of Fallot. Circulation 27:796–800

    Google Scholar 

  • Ionescu MI, Tandon AP, Macartney FJ (1979) Long-term sequential hemodynamic evaluation of right ventricular outflow tract reconstruction using a valve mechanism. Ann Thorac Surg 27:426–434

    CAS  PubMed  Google Scholar 

  • lyer KS, Mee RB (1991) Staged repair of pulmonary atresia with ventricular septal defect and major systemic to pulmonary artery collaterals. Ann Thorac Surg 51:65–72

    Google Scholar 

  • Johnson RJ, Haworth SG (1982) Pulmonary vascular and alveolar development in tetralogy of Fallot: a recommendation for early correction. Thorax 37:893–901

    CAS  PubMed  Google Scholar 

  • Jonas RA (1998) The arterial switch operation for transposition of the great arteries. Operative techniques in thoracic and cardiovascular surgery: A comparative atlas 3:238–253

    Google Scholar 

  • Jonas RA (2004) Comprehensive surgical management of congenital heart disease. Hodders Arnold, London

    Google Scholar 

  • Kawashima Y, Fujita T, Miyamoto T, Manabe H (1971) Intraventricular rerouting of blood for the correction of Taussig-Bing malformation. J Thorac Cardiovasc Surg 62:825–829

    CAS  PubMed  Google Scholar 

  • Kawashima Y, Matsuda H, Hirose H et al. (1985) Ninety consecutive corrective operations for tetralogy of Fallot with or without minimal right ventriculotomy. J Thorac Cardiovasc Surg 90:856–863

    CAS  PubMed  Google Scholar 

  • Kilner PJ, Sievers B, Meyer GP, Ho SY (2002) Double-chambered right ventricle or sub-infundibular stenosis assessed by cardiovascular magnetic resonance. J Cardiovasc Magn Reson 4:373–379

    PubMed  Google Scholar 

  • Kim N, Friedberg MK, Silverman NH (2006) Diagnosis and prognosis of fetuses with double outlet right ventricle. Prenat Diagn 26:740–745

    PubMed  Google Scholar 

  • Kim WH, Seo JW, Kim SJ et al. (2005) Aortic dissection late after repair of tetralogy of Fallot. Int J Cardiol 101:515–516

    PubMed  Google Scholar 

  • Kirklin JW, DuShane JW, Patrick RT et al. (1955) Intra cardiac surgery with the aid of a mechanical pump-oxygenator system (Gibbon type): report of eight cases. Proc Staff Meet Mayo Clin 18:201–206

    Google Scholar 

  • Kirshbom PM, Kogon BE (2004) Tetralogy of Fallot with absent pulmonary valve syndrome. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 7:65–71

    PubMed  Google Scholar 

  • Klinner W, Pasini M, Schaudig A (1962) Anastomose zwischen System und Lungenarterie mit Hilfe von Kunststoffprothesen bei cyanotischen Herzvitien. Thoraxchirurgie 10:68–75

    CAS  PubMed  Google Scholar 

  • Klinner W, Reichart B (1991) Korrektur des gemeinsamen Abgangs der großen Gefäße v om rechten Ventrikel. In: Borst HG, Klinner W, Oelert H (Hrsg.) Herzchirurgie. Springer, Berlin Heidelberg New York Tokio, S. 205–209

    Google Scholar 

  • Klinner W, Zenker R (1965) Experience with correction of Fallot’s Tetralogy in 178 cases. Surgery 57:353–257

    CAS  PubMed  Google Scholar 

  • Kouchoukos NT, Blackstone EH, Doty DB, Hanley FL, Karp RB (2003) Kirklin/ Barratt Boyes cardiac surgery, 3rd edn. Churchill Livingstone, Philadelphia, p 982

    Google Scholar 

  • Lacour-Gayet F (2008) Intracardiac repair of double outlet right ventricle. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu: 39–43

    Google Scholar 

  • Laks H, Gates RN, Grant PW et al. (1995) Aortic to right ventricular shunt for pulmonary atresia and intact ventricular septum. Ann Thorac Surg 59:342–347

    CAS  PubMed  Google Scholar 

  • Laks H, Plunket MD (2001) Surgical management of pulmonary atresia with intact ventricular septum. Progr Pediatr Cardiol 13:183–197

    Google Scholar 

  • Lecompte Y, Bex JP (1985) Repair of transposition of the great arteries with ventricular septal defect and left ventricular outflow tract obstruction. J Thorac Cardiovasc Surg 90:151–152

    CAS  PubMed  Google Scholar 

  • Lev M, Bharati S, Meng CC et al. (1972) A concept of double-outlet right ventricle. J Thorac Cardiovasc Surg 64:271–281

    CAS  PubMed  Google Scholar 

  • Lillehei C W, Cohen M, Warden HE et al. (1955) Direct vision intracardiac surgical correction of the tetralogy of Fallot, pentalogy of Fallot, and pulmonary atresia defects; report of first ten cases. Ann Surg 142:418–442

    CAS  PubMed  Google Scholar 

  • Lofland GK (2004) Pulmonary atresia, ventricular septal defect, and multiple aorta pulmonary collateral arteries. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 7:85–94

    PubMed  Google Scholar 

  • Luciani GB, Wells WJ, Khong A, Starnes VA (1997) The clamshell incision for bilateral pulmonary artery reconstruction in tetralogy of Fallot with pulmonary atresia. J Thorac Cardiovasc Surg 113:443–452

    CAS  PubMed  Google Scholar 

  • Luhmer I, Ziemer G (1993) Coarctation of the pulmonary artery in neonates. Prevalence, diagnosis, and surgical treatment. J Thorac Cardiovasc Surg 106:889–894

    CAS  PubMed  Google Scholar 

  • Lurz P, Bonhoeffer P (2008) Percutaneous implantation of pulmonary valves for treatment of right ventricular outflow tract dysfunction. Cardiol Young 18:260–267

    PubMed  Google Scholar 

  • Mackie AS, Gauvreau K, Perry SB, del Nido PJ, Geva T (2003) Echocardiography predictors of aortopulmonary collaterals in infants with tetralogy of fallot and pulmonary atresia. J Am Coll Cardiol 41: 852–857

    PubMed  Google Scholar 

  • McElhinney DB, Chatterjee KM, Reddy VM (2000) Double-chambered right ventricle presenting in adulthood. Ann Thorac Surg 70:124–127

    CAS  PubMed  Google Scholar 

  • McElhinney DB, Parry AJ, Reddy VM, Hanley FL, Stanger P (1998a) Left pulmonary artery kinking caused by outflow tract dilatation after transanular patch repair of tetralogy of Fallot. Ann Thorac Surg 5: 1120–1126

    Google Scholar 

  • McElhinney DB, Reddy VM, Silverman NH, Brook MM, Hanley FL (1998b) Atrioventricular septal defect with common valvar orifice and tetralogy of Fallot revisited: making a case for primary repair in infancy. Cardiol Young 8:455–461

    CAS  PubMed  Google Scholar 

  • Mearns AJ, Deverall PB, Kester RC (1978) Revascularization of an arm for incipient gangrene after Blalock-Taussig anastomosis. Br J Surg 65: 467–468

    CAS  PubMed  Google Scholar 

  • Meyns B, Van Garsse L, Boshoff D et al. (2004) The Contegra conduit in the right ventricular outflow tract induces supravalvular stenosis. J Thorac Cardiovasc Surg 128:834–840

    PubMed  Google Scholar 

  • Milanesi O, Talenti E, Pellegrino PA, Thiene G (1984) Abnormal pulmonary artery branching in tetralogy of Fallot with “absent” pulmonary valve. Int J Cardiol 6:375–380

    CAS  PubMed  Google Scholar 

  • Moran AM, Hornberger LK, Jonas RA, Keane JF (1998) Development of a double-chambered right ventricle after repair of tetralogy of Fallot. J Am Coll Cardiol 31:1127–1133

    CAS  PubMed  Google Scholar 

  • Moritz A, Marx M, Wollenek G, Domanig E, Wolner E (1996) Complete repair of PA-VSD with diminutive or discontinuous pulmonary arteries by transverse thoracosternotomy. Ann Thorac Surg 61:646–650

    CAS  PubMed  Google Scholar 

  • Najm HK, Van Arsdell GS, Watzka S et al. (1998) Primary repair is superior to initial palliation in children with atrioventricular septal defect and tetralogy of Fallot. J Thorac Cardiovasc Surg 116:905–913

    CAS  PubMed  Google Scholar 

  • Nakata S, Imai Y, Takanashi Y et al. (1984) A new method for the quantitative standardization of cross-sectional areas of the pulmonary arteries in congenital heart diseases with decreased pulmonary blood flow. J Thorac Cardiovasc Surg 88:610–619

    CAS  PubMed  Google Scholar 

  • Norgård G, Gatzoulis MA, Moraes F et al. (1996) Relationship between type of outflow tract repair and postoperative right ventricular diastolic physiology in tetralogy of Fallot. Implications for longterm outcome. Circulation 94:3276–3280

    PubMed  Google Scholar 

  • Nørgaard MA, Alphonso N, Cochrane AD et al. (2006) Major aorto-pulmonary collateral arteries of patients with pulmonary atresia and ventricular septal defect are dilated bronchial arteries. Eur J Cardiothorac Surg 29:653–658

    PubMed  Google Scholar 

  • Parry AJ, McElhinney DB, Kung GC et at. (2000) Elective primary repair of acyanotic tetralogy of Fallot in early infancy: overall outcome and impact on the pulmonary valve. J Am Coll Cardiol 36:2279–2283

    CAS  PubMed  Google Scholar 

  • Parsons JM, Rees MR, Gibbs JL (1991) Percutaneous laser valvotomy with balloon dilatation of the pulmonary valve as primary treatment for pulmonary atresia. Br Heart J 66:36–38

    CAS  PubMed  Google Scholar 

  • Patrick DL, McGoon DC (1968) An operation for double-outlet right ventricle with transposition of the great arteries. J Cardiovasc Surg (Torino) 9:537–542

    CAS  Google Scholar 

  • Pawade A, Capuani A, Penny DJ, Karl TR, Mee RB (1993) Pulmonary atresiawith intactventricularseptum:surgical management based on right ventricular infundibulum. J Card Surg 8:371–383

    CAS  PubMed  Google Scholar 

  • Pfaundler M, Schlossmann A (1926) Handbuch der Kinderheilkunde, 4. Aufl. Bd IĪV. Vogel, Leipzig

    Google Scholar 

  • Planche C, Lacour-Gayet F, Serraf A (1998) Arterial switch. Pediatr Cardiol 19:297–307

    CAS  PubMed  Google Scholar 

  • Plunkett MD, Bond LM, Geiss DM (1998) Use of the “chimney patch” technique for Norwood stage I procedures. Ann Thorac Surg 66: 1438–1439

    CAS  PubMed  Google Scholar 

  • Preminger TJ, Sanders SP, van der Velde ME, Casta ñeda AR, Lock JE (1994) “Intramural” residual interventricular defects after repair of conotruncal malformations. Circulation 89:236–242

    CAS  PubMed  Google Scholar 

  • Potts WD, Smith S, Gibson S (1946) Anastomosis of the aorta to a pulmonary artery for certain types of congenital heart disease. JAMA 132: 629

    Google Scholar 

  • Puga FJ, Leoni FE, Julsrud PR, Mair DD (1989) Complete repair of pulmonary atresia, ventricular septal defect, and severe peripheral arborization abnormalities of the central pulmonary arteries. Experience with preliminary unifocalization procedures in 38 patients. J Thorac Cardiovasc Surg 98:1018–1028

    CAS  PubMed  Google Scholar 

  • Puga FJ, McGoon DC, Julsrud PR, Danielson GK, Mair DD (1983) Complete repair of pulmonary atresia with nonconfluent pulmonary arteries. Ann Thorac Surg 35:36–44

    CAS  PubMed  Google Scholar 

  • Quaegebeur JM (1986) The arterial Switch operation. Rationale, results, and perspectives. Thesis. Leiden University, The Netherlands

    Google Scholar 

  • Qureshi SA, Kirk CR, Lamb RK, Arnold R, Wilkinson JL (1988) Balloon dilatation of the pulmonary valve in the first year of life in patients with tetralogy of Fallot: a preliminary study, Br Heart J 60:232–235

    CAS  PubMed  Google Scholar 

  • Rabinovitch M, Grady S, David I et al. (1982) Compression of intrapulmonary bronchi by abnormally branching pulmonary arteries associated with absent pulmonary valves. Am J Cardiol 50:804–813

    CAS  PubMed  Google Scholar 

  • Rabinovitch M, Herrera-deLeon V, Castaneda AR, Reid L (1981) Growth and development of the pulmonary vascular bed in patients with tetralogy of Fallot with or without pulmonary atresia. Circulation 64:1234–1249

    CAS  PubMed  Google Scholar 

  • Rastelli GC, Wallace RB, Ongley PA (1969) Complete repair of transposition of the great arteries with pulmonary stenosis. A review and report of a case corrected by using a new surgical technique. Circulation 39:83–95

    CAS  PubMed  Google Scholar 

  • Rathi VK, Doyle M, Williams RB et al. (2005) Massive aortic aneurysm and dissection in repaired tetralogy of Fallot; diagnosis by cardiovascular magnetic resonance imaging. Int J Cardiol 101:169–170

    PubMed  Google Scholar 

  • Razzouk AJ, Freedom RM, Cohen AJ et al. (1992) The recognition, identification of morphologic substrate, and treatment of subaortic stenosis after a Fontan operation. An analysis of twelve patients. J Thorac Cardiovasc Surg 104:1750–1753

    Google Scholar 

  • Reddy VM, Liddicoat JR, Hanley FL (1995) Midline one-stage complete unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. J Thorac Cardiovasc Surg 109:832–844

    CAS  PubMed  Google Scholar 

  • Reddy VM, Petrossian E, McElhinney DB et al. (1997) One-stage complete unifocalization in infants: when should theventricularseptal defect be closed? J Thorac Card iovasc Surg 113:858–866

    CAS  Google Scholar 

  • Redington AN (2006) Physiopathology of right ventricular failure. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu: 3–10

    Google Scholar 

  • Rome JJ, Mayer JE, Castaneda AR, Lock JE (1993) Tetralogy of Fallot with pulmonary atresia. Rehabilitation of diminutive pulmonary arteries. Circulation 88:1691–1698

    CAS  PubMed  Google Scholar 

  • Rychik J, Levy H, Gaynor JW, DeCampli WM, Spray TL (1998) Outcome after operations for pulmonary atresia with intact ventricular septum. J Thorac Cardiovasc Surg 116:924–931

    CAS  PubMed  Google Scholar 

  • Sachweh J, Däbritz S, Didilis V et al. (1998) Pulmonary artery stenosis after systemic-to-pulmonary shunt operations. Eur J Cardiothorac Surg 14:229–234

    CAS  PubMed  Google Scholar 

  • Sandifort E (1777) Observationes anatomico pathologicae, caput primum. Eyk et Vygh, Lugduni Batavorum, pp 1–38

    Google Scholar 

  • Sawatari K, Imai Y, Kurosawa H, Isomatsu Y, Momma K (1989) Staged operation for pulmonary atresia and ventricular septal defect with major aortopulmonary collateral arteries. New technique for complete unifocalization. J Thorac Cardiovasc Surg 98:738–750

    CAS  PubMed  Google Scholar 

  • Schreiber C, Bauernschmitt R, Augustin N (2006) Implantation of a prosthesis mounted inside a self-expandable stent in the pulmonary valvular area without use of cardiopulmonary bypass. Ann Thorac Surg 81:e1–e3

    PubMed  Google Scholar 

  • Sellors TH (1948) Surgery of pulmonary stenosis; a case in which the pulmonary valve was successfully divided. Lancet 26:988

    Google Scholar 

  • Shaddy RE, Sturtevant JE, Judd VE, McGough EC (1990) Right ventricular growth after transventricular pulmonary valvotomy and central aortopulmonary shunt for pulmonary atresia and intact ventricular septum. Circulation 82:SIV157–SIV163

    Google Scholar 

  • Shanley CJ, Lupinetti FM, Shah NL et al. (1993) Primary unifocalization for the absence of intrapericardial pulmonary arteries in the neonate. J Thorac Cardiovasc Surg 106:237–247

    CAS  PubMed  Google Scholar 

  • Shimazaki Y, Blackstone EH, Kirklin JW (1984) The natural history of isolated congenital pulmonary valve incompetence: surgical implications. Thorac Cardiovasc Surg 32:257–259

    CAS  PubMed  Google Scholar 

  • Skovránek J, Goetzová J, Samánek M (1976) Changes in muscle blood flow and development of the arm following the Blalock-Taussig anastomosis. Cardiology 61:131–137

    PubMed  Google Scholar 

  • Sluysmans T, Neven B, Rubay J et al. (1995) Early balloon dilatation of the pulmonary valve in infants with tetralogy of Fallot. Risks and benefits. Circulation 91:1506–1511

    CAS  PubMed  Google Scholar 

  • Sokól S, Narkiewicz M, Billewicz OJ (1969) Subclavian steal syndrome after Blalock-Taussig anastomoses. Cardiovasc Surg (Torino) 10: 350–354

    Google Scholar 

  • Stellin G, Jonas RA, Goh TH, Brawn WJ, Venables AW, Mee RB (1983) Surgicaltreatment of absent pulmonary valve syndrome in infants: relief of bronchial obstruction. Ann Thorac Surg 36:468–475

    CAS  PubMed  Google Scholar 

  • Stellin G, Milanesi O, Rubino M et al. (1995) Repair of tetralogy of Fallot in the first six months of life: transatrial versus transventricular approach. AnnThorac Surg 60:S588–S591

    CAS  Google Scholar 

  • Stenonis DN (1671) Embryo monstro affinis Parisii dissect us. In: Bartholini T (ed) Acta Medica et Philosophica Hafniensia. Petrus Haubold, Kopenhagen, pp 200–203

    Google Scholar 

  • Sullivan ID, Wren C, Stark J et al. (1988) Surgical unifocalization in pulmonary atresia and ventricular septal defect. A realistic goal? Circulation 78:1115–11113

    Google Scholar 

  • Suzuki K, Ho SY, Anderson RH et al. (1998a) Morphometric analysis of atrioventricular septal defect with common valve orifice. J A m Coll Cardiol 31:217–223

    CAS  Google Scholar 

  • Suzuki K, Ho SY, Anderson RH et al. (1998b) Interventricular communication in complete atrioventricular septal defect. Ann Thorac Surg 66: 1389–1393

    CAS  PubMed  Google Scholar 

  • Takabayashi S, Shimpo H, Miyake Y, Onoda K, Amano H, Maruyama K (2005) Postoperative prone position management of tetralogy of Fallot with absent pulmonary valve syndrome. Jpn J Thorac Cardiovasc Surg 53:150–153

    PubMed  Google Scholar 

  • Tan JL, Gatzoulis MA, Ho SY (2006) Aortic root disease in tetralogy of Fallot. Curr Opin Cardiol 21:569–572

    PubMed  Google Scholar 

  • Tanaka AC, Atik E, Ikari NM et al. (1993) Transposition of the great arteries with posterior aorta. Arq Bras Cardiol 60:339–342

    CAS  PubMed  Google Scholar 

  • Taussig HB (1948) Tetra logy of Fallot especially the care of the cyanotic infant and child. Pediatrics 1:307

    CAS  PubMed  Google Scholar 

  • Taussig HB, Bing RJ (1949) Complete transposition of the aorta and a levoposition of the pulmonary artery; clinical, physiological, and pathological findings. Am Heart J 37:551–559

    CAS  PubMed  Google Scholar 

  • Thiene G, Bortolotti U, Gallucci V, Valente ML, Volta SD (1977) Pulmonary atresia with ventricular septal defect. Further anatomical observations, Br Heart J 39:1223–1233

    CAS  PubMed  Google Scholar 

  • Van Praagh R (1968) What is the Taussig-Bing malformation? Circulation 38:445–449

    PubMed  Google Scholar 

  • Van Praagh R (1989) Etienne-Louis Arthur Fallot and histetralogy:a new translation of Fallot’s summary and a modern reassessment of this anomaly. Eur J Cardio-Thorac Surg 3:381–386

    Google Scholar 

  • Van Praagh R, Perez-Trevino O, Lopez-Cuellar M et al. (1971) Transposition of the great arteries with posterior aorta, anterior pulmonary artery, subpulmo nary conus and fibrous continuity between aortic and atrioventricular valves. Am J Cardiol 28:621–631

    PubMed  Google Scholar 

  • Van Praagh R, Van Praagh S, Nebesar RA, Muster AJ, Sinha SN, Paul MH (1970) Tetralogy of Fallot: underdevelopment of the pulmonary infundibulum and its sequelae. Am J Cardiol 26:25–33

    PubMed  Google Scholar 

  • Vishnevsky A, Donetsky D (1960) A new method of the creation of the interarterial anastomosis in patients with the congenital cyanotic heart defects. Khirurgia 36:39–42

    Google Scholar 

  • Waldman JD, Lamberti JJ, Mathewson JW, George L (1984) Surgical closure of the tricuspid valve for pulmonary atresia, intact ventricular septum, and right ventricle to coronary artery communications. Pediatr Cardiol 5:221–223

    CAS  PubMed  Google Scholar 

  • Waterston DJ (1962) Treatment of Fallot’s tetralogy in children under 1 year of age. Rozhl Chir 41:181–183

    CAS  PubMed  Google Scholar 

  • Watterson KG, Wilkinson JL, Karl TR, Mee RB (1991) Very small pulmonary arteries: central end-to-side shunt. Ann Thorac Surg 52:1132–1137

    CAS  PubMed  Google Scholar 

  • Wilkinson JL, Arnold R, Anderson RH, Acerete F (1975) “Posterior” transposition reconsidered. Br Heart J 37:757–766

    CAS  PubMed  Google Scholar 

  • Williams WG, Burrows P, Freedom RM et al. (1991) Thromboexclusion of the right ventricle in children with pulmonary atresia and intact ventricular septum, J Thorac Cardiovasc Surg 101:222–229

    CAS  PubMed  Google Scholar 

  • Wong PC, Sanders SP, Jonas RA et al. (1991) Pulmonary valve-moderator band distance and association with development of double-chambered right ventricle. Am J Cardiol 68:1681–1686

    CAS  PubMed  Google Scholar 

  • Yagihara T, Yamamoto F, Nishigaki K et al. (1996) Unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. Thorac Cardiovasc Surg 112:392–402

    CAS  Google Scholar 

  • Zach M, Beitzke A, Singer H, Höfler H, Schellmann B (1979) The syndrome of absent pulmonary valve and ventricular septal defect — anatomical features and embryological implications. Basic Res Cardiol 74:54–68

    CAS  PubMed  Google Scholar 

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  1. Klinik für Thorax-, Herz- und Gefäßchirurgie, Eberhard-Karls-Universität Tübingen, Hoppe-Seyler-Str. 3, 72076, Tübingen

    Prof. Dr. med. Dr. h.c. G. Ziemer & Dr. med. Z. Nagy

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Ziemer, G., Nagy, Z. (2010). Angeborene Herzfehler mit Anomalien des rechtsventrikulären Ausflusstrakts. In: Herzchirurgie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-79713-5_13

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